Vasculitis diagnosis | Number N = 304 | Frequencies per 100,000 histological specimens | Percentages | |
---|---|---|---|---|
 |  |  | groups of vasculitis | subgroups of vasculitis |
I. Primary vasculitis | 142 | 74 | 46.7 | Â |
   A. Affecting large, medium and small sized blood vessels | 1 | 0.6 |  | 0.7 |
1. Giant cell (Temporal) arteritis | 1 | 0.6 | Â | Â |
   B. Affecting predominantly medium and small-sized blood vessels | 29 | 17.5 |  | 20.4 |
1. Polyarteritis nodosa | 24 | 14.5 | Â | Â |
2. Churg-Strauss syndrome | 2 | 1.2 | Â | Â |
3. Wegener's granulomatosis | 3 | 1.8 | Â | Â |
   C. Affecting predominantly small-sized blood vessels | 74 | 44.7 |  | 52.1 |
1. Microscopic polyangiitis | 1 | 0.6 | Â | Â |
2. Henoch-Schönlein purpura | 9 | 5.4 |  |  |
3. Cutaneous leukocytoclastic angiitis | 64 | 38.7 | Â | Â |
   D. Miscellaneous conditions | 38 | 23 |  | 26.8 |
1. Buerger's disease | 38 | 23 | Â | Â |
II. Secondary vasculitides | 55 | 33.2 | 18.1 | Â |
1. Infection-related vasculitis | 20 | 12.1 | Â | Â |
2. Connective tissue disease vasculitis | 33 | 20 | Â | Â |
3. Hypocomplementemic urticarial vasculitis | 1 | 0.6 | Â | Â |
4. Vasculitis associated with neoplasia | 1 | 0.6 | Â | Â |
III. Unclassified vasculitis | 107 | 64.6 | 35.2 | Â |
Total | 304 | 183.6 | 100 | Â |