Vasculitis diagnosis | Number N = 304 | Frequencies per 100,000 histological specimens | Percentages | |
---|---|---|---|---|
 |  |  | groups of vasculitis | subgroups of vasculitis |
1. Leukocytoclastic vasculitis | 107 | 64.6 | 35.2 | Â |
   1.1. Erythema elevatum diutinum | 1 | 0.6 |  | 0.9 |
   1.2. Secondary to diseases | 42 | 25.4 |  | 39.3 |
1.2.1. SLE | 14 | 8.5 | Â | Â |
1.2.2. PM/DM | 14 | 8.5 | Â | Â |
1.2.3. Diffuse/limited scleroderma | 5 | 6.7 | Â | Â |
1.2.4. Henoch-Schönlein purpura | 9 | 5.4 |  |  |
   1.3 Livedoid leukocytoclastic vasculitis | 5 | 3 |  | 4.7 |
   1.4. Idiopathic | 59 | 35.6 |  | 55.1 |
2. Lymphomonocitic's vasculitis | 53 | 32 | 17.4 | Â |
   2.1. Schamberg's purpura | 1 | 0,6 |  | 1.9 |
   2.2. Chronic urticaria, associated | 1 | 0.6 |  | 1.9 |
   2.3. Idiopathic | 51 | 30.8 |  | 96.2 |
3. Nodular vasculitis | 19 | 11.5 | 3.6 | Â |
   3.1. Erythema nodosum | 7 | 4.2 |  | 36.8 |
   3.2. Granulomatous panniculitis | 2 | 1.2 |  | 10.5 |
   3.3. Vasculitis in panniculitis | 4 | 2.4 |  | 21.1 |
   3.4. Idiopathic | 6 | 3.6 |  | 31.6 |
4. Granulomatous vasculitis | 11 | 6.6 | 3.6 | Â |
   4.1. Wegener's granulomatosis | 3 | 1.8 |  | 27.3 |
   4.2. Churg Strauss | 2 | 1.2 |  | 18.2 |
   4.3. Lymphomatoid granulomatosis (lung) | 1 | 0.6 |  | 9.1 |
   4.4. Granuloma annulare | 1 | 0.6 |  | 9.1 |
   4.5. Giant cell (Temporal) arteritis | 1 | 0.6 |  | 9.1 |
   4.6. Idiopathic | 3 | 1.8 |  | 27.3 |
5. Polyarteritis nodosa | 24 | 14.5 | 7.9 | Â |
   5.1. Generalized | 16 | 4.8 |  | 66.7 |
   5.2. Cutaneous | 8 | 9.7 |  | 33.3 |
6. Vasculitis like diseases | 4 | 2.4 | 1.3 | Â |
   6.1. Arterio-embolism | 4 | 2.4 |  | 100 |
7. Infection-related vasculitis | 20 | 12.1 | 6.6 | Â |
   7.1. Mycobacterium | 12 | 7.2 |  | 60 |
   7.2. Bacterial infections | 8 | 4.8 |  | 40 |
8. Microscopic polyangiitis | 1 | 0.6 | 0.3 | Â |
9. Thromboangiitis obliterans | 38 | 23 | 12.5 | Â |
10. Unclassified vasculitis | 27 | 16.3 | 8.9 | Â |
TOTAL | 304 | Â | 100 | Â |